Güncel Patoloji Dergisi
2019, Cilt 3, Sayı 1
Follicular Porokeratosis; Case Report and Review of the Literature
1 İstanbul Medipol Üniversitesi, Tıp Fakültesi, Patoloji Anabilim Dalı, İSTANBUL
2 Acıbadem Mehmet Ali Aydınlar Üniversitesi, Tıp Fakültesi, Patoloji Anabilim Dalı, İSTANBUL
DOI : 10.5146/jcpath.2019.45 Aim: Porokeratosis, a group of autosomal dominant inherited diseases characterized by disorder of epidermal keratinization. Follicular porokeratosis is a rare and newly described histological variant characterized by the formation of a limited cornoid lamella in the hair follicle orifices.
2 Acıbadem Mehmet Ali Aydınlar Üniversitesi, Tıp Fakültesi, Patoloji Anabilim Dalı, İSTANBUL
DOI : 10.5146/jcpath.2019.45 Aim: Porokeratosis, a group of autosomal dominant inherited diseases characterized by disorder of epidermal keratinization. Follicular porokeratosis is a rare and newly described histological variant characterized by the formation of a limited cornoid lamella in the hair follicle orifices.
Case: A 24 year-old female presented with slowly growing 0.3 cm in diameter brownish scaly papules on the right cheek and jaw. Microscopic examination of excisional biopsy specimens from both sites had porokeratotic column confined to the dilated hair follicle. The granular layer beneath the parakeratosis was absent and dyseratotic cells were observed in these areas. Histological findings were consistent with follicular porokeratosis.
Conclusion: The case of follicular porokeratosis was found to be worthy of presentation due to its rarity in the literature and a newly defined entity.
Anahtar Kelimeler : Follicular porokeratosis, Cornoid lamella, Hair follicle orifices