Güncel Patoloji Dergisi 2019, Cilt 3, Sayı 3
Recent Developments in Interstitial Lung Diseases
Funda DEMIRAĞ
1 Sağlık Bilimleri Üniversitesi, Atatürk Göğüs Hastalıkları ve Göğüs Cerrahisi Eğitim ve Araştırma Hastanesi, Tıbbi Patoloji Anabilim Dalı, ANKARA
DOI : 10.5146/jcpath.2019.56 Idiopathic interstitial pneumonia is a combination of histologically different amounts of fibrosis and inflammation. Therefore, a multidisciplinary council decision is recommended for diagnosis. A guide for clinical diagnosis of idiopathic pulmonary fibrosis, including clinical, radiological and histopathological data, has been published. In recent years, chronic hypersensitivity pneumonia has become prominent in the differential diagnosis of idiopathic pulmonary fibrosis. Pleuroparenchymal fibroelastosis, autoimmune interstitial pneumonia, combined pulmonary fibrosis and emphysema syndrome, fibrosing cryptogenic organized pneumonia, acute fibrinous and organized pneumonia are newly defined entities. In many interstitial lung diseases, telomere related genetic changes have been described and genetic features of interstitial lung diseases have been demonstrated. Anahtar Kelimeler : Interstitial lung disease, Classification, Idiopathic interstitial pneumonia, Pathology